Mature (peripheral) T neoplasms
T-cell chronic lymphocytic leukemia / small
lymphocytic lymphoma
T-cell prolymphocytic leukemia
T-cell granular lymphocytic leukemiaII
Aggressive NK leukemia
Adult T-cell lymphoma/leukemia (HTLV-1+)
Extranodal NK/T-cell lymphoma, nasal type#
Enteropathy-like T-cell lymphoma**
Hepatosplenic γδ T-cell lymphoma*
Subcutaneous panniculitis-like T-cell lymphoma*
Mycosis fungoides/Sézary syndrome
Anaplastic large cell lymphoma, T/null cell,
primary cutaneous type
Peripheral T-cell lymphoma, not otherwise characterized
Angioimmunoblastic T-cell lymphoma
Anaplastic large cell lymphoma, T/null cell,
primary systemic type
Hodgkin’s Lymphoma (Hodgkin’s Disease)
Nodular lymphocyte predominance Hodgkin’s lymphoma
Classic Hodgkin’s lymphoma
Nodular sclerosis Hodgkin’s lymphoma (grades 1 and 2)
Lymphocyte-rich classic Hodgkin’s lymphoma
Mixed cellularity Hodgkin’s lymphoma
Lymphocyte depletion Hodgkin’s lymphoma
† Not described in REAL classification
§ Includes the so-called Burkitt-like lymphomas
** Formerly known as intestinal T-cell lymphoma
# Formerly know as angiocentric lymphoma
100
75
50
25
0
0
2
4
6
8
10
H
HI
LI
L
Patients (%)
Year
100
60
40
20
0
0
2
5
6
7
8
3
4
1
80
IPI 0-1
IPI 2-3
IPI 4-5
P<0.001
Burkitt’s, FL, DLCL, HCL
ALL CLL, PLL
WM
MM
Hairy cell
Large cell
LP/Waldenström’s
Mantle cell
Marginal zone
Small cleaved
Adapted with permission from G.D. Maloney.
Mean channel fluorescence
Patients (%)
Year
100
80
60
40
20
0
0
1
2
3
4
5
6
CHOP
m-BACOD
ProMACE-CytaBOM
MACOP-B
Coiffier et al. N Engl J Med. 2002;346:235.
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